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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
60 %
Mots clés
Regulatory T cells
Dystrophie musculaire oculopharyngée
AChR antibodies
Metabolism
Annexin A2
Fibrosis
Muscle dystrophy
Effector T cells
Calcium
Muscle fibrosis
Gene therapy
DNA methylation
DMD
Oculopharyngeal muscular dystrophy
Antisens oligonucleotides
Human
PABPN1 agregates
Pax7
2-D PAGE
Thérapie génique
Intercellular communication
Dystrophin
Duchenne muscular dystrophy
ALS
AAV
DUX4
Neuromuscular junction NMJ
Geriatric assessment
Anti-acetylcholine receptor antibodies
FSHD
Regenerative medicine
Triplet expansion disease
Aged
Transcriptomics
Muscle
Satellite cells
RNA
Cell therapy
Autoimmune diseases
Gene replacement
AUTOPHAGY
Adipose tissue
Actin
Anti-fibrotic pharmacotherapies
Myopathies
Regeneration
Satellite cell
Neuromuscular disease
Mass spectrometry
GENE
ARN
Bile salt hydrolases
Differentiation
APOPTOSIS
Functional genomics
Myotube
Nuclear envelope
Antiserum
AAV vectors
Muscular dystrophy
Cross-bridge kinetics
Alzheimer's disease
Muscle strength
Akt
Alphavirus
Amyotrophic Lateral Sclerosis
Biomarker
Myoblast
MUTATIONS
Omics
Aggregate
Arbovirus
Lamins
Andermann syndrome
FAPs
Atrophy
Inflammation
Ageing
Dysferlin
Accelerometry
Myositis
Skeletal muscle
Autologous
BINDING SPECIFICITY
Exon-skipping
Sarcopenia
Muscle stem cells
Myogenesis
Xenograft
Epigenetics
Myoblasts
Myopathy
Myosin
Dysferlinopathy
PABPN1
Haploinsufficiency
OPMD
Agrégats de PABPN1
Pharyngeal muscle
Aav-U7